The evaluation of the disease advancement in patients with mucopolysaccharidosis
نویسنده
چکیده
Introduction One of the most important manifestations of mucopolysaccharidosis (MPS) type I, II and VI is a progressive disease of the osteoarticular system. The evaluation of the disease advancement is difficult due to the complexity of symptoms. The characteristic features are progressive limitation of joint mobility and joint pain. These symptoms affect the quality of patient life. A uniform scale has not been developed for these patients.
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عنوان ژورنال:
دوره 12 شماره
صفحات -
تاریخ انتشار 2014